Table 3 causes for pulmonary artery aneurysms without arteriovenous communication adapted from fischer et al 18. This condition is characterized by vasculitis, deep venous thrombosis and aneurysms that mainly involve the pulmonary arteries resulting in hemoptysis. Hughes stovin syndrome hss is a particularly rare disease characterized by multiple pulmonary artery andor bronchial artery aneurysms with concomitant peripheral venous thrombosis, and is believed to be a cardiovascular variant of behcets disease. Luckily, there are lots of free and paid tools that can compress a pdf file in just a few easy steps. B four weeks later asecond selective leftpulmonary angiogram demonstrates arapid increase inthe sizeoftheaneurysm arrow. Pdf hughesstovin syndrome is a rare disorder of unknown etiology characterized by the association of multiple pulmonary artery aneurysms and deep. Jan 29, 2009 background hughes stovin syndrome is a rare entity. Weber aa hughes stovin syndrome is a rare condition first described in 1959 1 and is characterized by multiple pulmonary aneurysms and peripheral venous thrombosis. Hughes stovin syndrome pdf hughes stovin syndrome is a rare autoimmune disorder of unknown cause that is characterized by the combination of multiple pulmonary artery aneurysms and.
Acaseofhughesstovin syndromeincompletebehcets disease. The response to treatment was very good and at the 12 months followup the patient was completely asymptomatic, with no new radiological. Case presentation we report the case of an 18 years old, greek male patient with hughes stovin syndrome, who initially presented with deep vein. The variant was first described in 1959 by british physicians john patterson hughes and peter george ingle stovin.
This syndrome was named in honor of two english doctors dr. Paravertelral small arrows and anterior large arrow external jugular veins are present. Hughes stovin syndrome, pulmonary artery aneurysms and deep venous thrombosis. Multiple, small paa warrant early immunosuppression. Indian journal of vascular and endovascular surgery hughes.
Massive hemoptysis and deep venous thrombosis presenting in a woman with hughes stovin syndrome. Pulmonary medium vessel vasculitis in an 11 year old boy. Jan 01, 2016 hughes stovin syndrome is a lifethreatening disorder of unknown etiology. Hughes stovin syndrome hss is a rare autoimmune disorder of unknown etiology, characterized by peripheral deep venous thrombosis dvt and pulmonary andor bronchial aneurysms. Hughesstovin syndrome with pulmonary angiitis and focal. The etiopathogenesis of hughes stovin syndrome remains unexplained. Background hughes stovin syndrome is a rare entity. Pdf is a hugely popular format for documents simply because it is independent of the hardware or application used to create that file. The hughesstovin syndrome consists of deep venous thrombosis often involving the caval vein accompanied by single or multiple pulmonary arterial aneurysms. Intracardiac thrombus occurring as a thrombotic manifestation of hss is an unusual presentation and represents a challenge in diagnosis and. Hemoptysis, pulmonary aneurysm, hughes stovin syndrome 1. Typical symptoms are recurrent fever, chills, haemoptysis and coughs. But the radiologic suspicions were of neo plastic lesions. Apr, 2011 hughesstovin syndrome hss is a very rare clinical disorder characterized by thrombophlebitis and multiple pulmonary andor bronchial aneurysms.
Thursday, may 21, 2020 breaking news 5mo380r datasheet pdf. Ct angiography of pulmonary artery aneurysms in hughesstovin. This means it can be viewed across multiple devices, regardless of the underlying operating system. Introduction hughes stovin syndrome is a rare pathology associating pulmonary artery aneurysms and deep vein thrombosis and affecting commonly the young patient with a masculine predominance 1 2. Surgical resection provides an effective treatment option for patients with.
Hughesstovin syndrome orphanet journal of rare diseases. Cureus hughes stovin syndrome, a rare form of behcets. Hughes stovin syndrome is a rare disorder of unknown etiology characterized. You can use the tools in paint to add something to a different document. Once youve done it, youll be able to easily send the logos you create to clients, make them available for download, or attach them to emails in a fo. The exact etiology and pathogenesis of hss is unknown. Hughes stovin syndrome, heamoptysis, aneurysm introduction hughes stovin syndrome hss was first described in 1959 1. To combine pdf files into a single pdf document is easier than it looks. If your scanner saves files as pdf portbale document format files, the potential exists to merge the individual files into one doc. Stovin syndrome and was the first female case of typical hughes. Pathogenesis, imaging investigation and treatment of this syndrome are also briefly discussed. We report the case of an 18 years old, greek male patient with hughes stovin syndrome, who initially presented with deep vein. It is a rare variant of behcets disease, which entails more general problems with the circulatory system.
Is hughesstovin syndrome a particular expression of. Hughes stovin syndrome is a rare clinical condition characterized by multiple pulmonary artery aneurysms and peripheral venous thrombosis, first described in 1. This is a temporary file and hence do not link it from a website, instead link the url of this page if you wish to link the pdf file. Hughes stovin syndrome is a rare autoimmune disorder of unknown cause that is characterized by the combination of multiple pulmonary artery aneurysms and. It also aids in assessment of angiodysplastic bronchial arteries in hss. The aetiology of hughes stovin syndrome is still unknown and the natural course of the. Other associated features reported in hughes stovin syndrome include fever and elevated intracranial hypertension since its first description, there have been only a few reports of its occurrence in the english medical literature 2. Please visit the project page for details or ask questions at wikipedia talk. Most patients are young adult males between the age of 2040. Successful treatment of refractory hughes stovin syndrome. This method requires a graphics editor that can handle transparent images, in order to avoid white squares around the organs when pasting onto the body image. Massive pulmonary hemorrhage caused by rupture of an aneurysm is a frequent terminal event.
This article explains what pdfs are, how to open one, all the different ways. Pdf file or convert a pdf file to docx, jpg, or other file format. Multiple pulmonary arterial aneurysms in behcets disease and hughes stovin syndrome. Hughes stovin syndrome hss is a lifethreatening disorder, believed to be a. Less than 40 published cases of hss have been described in. Stovin syndrome is an exceedingly rare disorder consisting of multiple pulmonary aneurysms and peripheral venous thrombosis. Derive from scratch by this method, body diagrams can be derived by pasting organs into one of the plain body images shown below. Less than 40 published cases of hss have been described in english medical literature so far. An external file that holds a picture, illustration, etc. A pdf portable document format is a widely popular type of document format created by adobe. Hughesstovin syndrome hss is a very rare clinical disorder characterized by thrombophlebitis and multiple pulmonary andor bronchial aneurysms.
New approach cessful cyclophosphamide therapy with complete reso in the diagnosis of and therapy for hughes stovin syn lution of pulmonary artery aneurysm in hughes stovin drome. The aetiology of hughes stovin syndrome is still unknown and the natural course of the illness is usually fatal. Adobe systems is a software manufacturer that has created many document and multimedia editing programs. The true existence of this syndrome as a distinct clinical entity has been much debated, with some authors favoring hughes stovin as a. Hughes stovin syndrome hss is a very rare clinical disorder with less than 40 cases published in the english literature so far 1. His vital signs including temperature, arterial pressure and heart rate were normal. Treatment of chronic oral infections impacts long term prognosis of disease positively. Here we report the case of a 53yearold man with bilateral pulmonary artery aneurysms and lowerlimb dvt who developed massive hemoptysis. Durieux p, bletry o, huchon g, wechsler b, chretien j, godeau p. Hughes stovin syndrome is a rare autoimmune disorder of unknown cause that is characterized by the combination of multiple pulmonary artery aneurysms and deep vein thromboses. Hughes stovin syndrome hss is a very rare clinical disorder characterized by pulmonary artery aneurysms and peripheral venous thrombosis. Indian journal of vascular and endovascular surgery. Hughesuvstovinuv syndrom je vzacne onemocneni neznameho puvodu, ktere je charakterizovano kombinaci mnohocetnych aneurysmat plicnich arterii a hlubokou zilni trombozou.
Patients affected by this syndrome are often young adult men in the second to fourth decade of life. The paint program can help you make new image files, but it cannot open document or pdf file. A case of hughes stovin syndrome associated with hyperhomocysteinemia. Symptoms include recurrent dvt, cough, dyspnea, fever, chest pain and haemoptysis. By michelle rae uy 24 january 2020 knowing how to combine pdf files isnt reserved. Life threatening hemoptysis from hughes stovin syndrome. Hughes stovin syndrome may be partially manifested behcets syndrome 5. Earlier diagnosis could be in some cases crucial, allowing the prevention of the development of potentially lifethreatening pulmonary artery aneurysms 9. It has been described in literature less than 40 times. Depending on the type of scanner you have, you might only be able to scan one page of a document at a time. Hughes stovin syndrome have almost always been diag nosed at autopsy, except the hughes stovin first easel and kopp and greens case, where lobectomies have been done.
Bronchoscopy is often done in hss patients who present with hemoptysis. Hughes stovin syndrome umair khalid and taimur saleem abstract hughes stovin syndrome hss is a very rare clinical disorder characterized by thrombophlebitis and multiple pulmonary andor bronchial aneurysms. Pathologic studies of hughes stovin syndrome have repeatedly shown mural thrombus and inflammation, and many of the reports of pulmonary manifestations of behcets syndrome have suggested that an intraluminal clot in the pulmonary arteries might evolve. Hughes stovin syndrome shs is a pathology of unknown etiology with a lethal potential. Hughes stovin syndrome, described in 1959, is a rare disease characterized by multiple pulmonary artery aneurysms and peripheral venous thrombosis. The exact etiopathogenesis in hughes stovin syndrome is unrecognized 2 3. A pdf file is a portable document format file, developed by adobe systems. Making a pdf file of a logo is surprisingly easy and is essential for most web designers. The natural course of the illness is usually fatal because of fulminant haemoptysis.
Hughes stovin syndrome pdf hughes stovin syndrome is a rare autoimmune disorder of unknown cause that is characterized by the combination of multiple pulmonary artery aneurysms and friends of pdf all our visitors are our friends. Typical symptoms are recurrent fever, chills, haemoptysis and it usually affects young men. Any information contained in this pdf file is automatically generated from digital material. Read on to find out just how to combine multiple pdf files on macos and windows 10. Hughes stovin syndrome hss is a particularly rare disease characterized by multiple pulmonary artery andor bronchial artery aneurysms with concomitant peripheral venous thrombosis and is believed to be a cardiovascular variant of behcets disease. Hughes stovin syndrome hss is a very rare clinical disorder characterized by. Anteroposterior andblateral selective right internal jugular venograms.
In 1959, the two doctors described for the first time the syndrome as the association between deep vein thrombosis. The catheter isin the internal jugular vein arrowheads. Since its first description by hughes and stovin in 1959, there have been hughes stovin syndrome is a rare autoimmune disorder of unknown cause that is characterized by the combination of multiple pulmonary artery aneurysms and. This article is within the scope of wikiproject medicine, which recommends that medicinerelated articles follow the manual of style for medicinerelated articles and that biomedical information in any article use highquality medical sources. I paid for a pro membership specifically to enable this feature. One of the fun things about computers is playing with programs like paint. Less than 50 cases has been published in the literature, most. Unusual right ventricular thrombus in a woman with hughes stovin syndrome. It is a very rare disease characterized by deep vein thrombosis and pulmonary andor bronchial artery aneurysms. It is characterized by a combination of systemic venous thrombosis and pulmonary artery aneurysm. Hughes stovin syndrome is a very rare clinical entity characterized by pulmonary artery aneurysms and deep vein thrombosis dvt. An oversized pdf file can be hard to send through email and may not upload onto certain file managers. Sep 04, 2019 hughes stovin syndrome pdf september 4, 2019 0 comment hughesstovin syndrome is a rare autoimmune disorder of unknown cause that is characterized by the combination of multiple pulmonary artery aneurysms and.
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